Paraneoplastic dermatomyositis with histopathology compatible with Sweet-type neutrophilic dermatosis

Authors

  • María Emilia Sívori Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina
  • Isabel Hidalgo Parra Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina
  • Mariana Demarchi Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina
  • Rosa Beatriz Conforti Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina
  • Graciela Cecilia Lozano San Isidro Pathology, Province of Buenos Aires, Argentina

DOI:

https://doi.org/10.47196/6cze1974

Keywords:

dermatomyositis, paraneoplastic dermatomyositis, neutrophilic dermatosis

Abstract

Dermatomyositis (DM) is an inflammatory myopathy of unknown origin that generally presents a nonspecific skin histology. However, some cases of DM have been recorded with histopathology in which a diffuse neutrophilic infiltrate is observed in the dermis. We present the case of a patient with paraneoplastic DM whose skin biopsy revealed features compatible with Sweet-type neutrophilic dermatosis.

Author Biographies

  • María Emilia Sívori, Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina

    Attending Physician in Dermatology

  • Isabel Hidalgo Parra, Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina

    Staff Dermatologist

  • Mariana Demarchi, Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina

    Staff Dermatologist

  • Rosa Beatriz Conforti, Petrona Villegas de Cordero Hospital, Buenos Aires Province, Argentina

    Dermatologist, Head of the Dermatology Service

  • Graciela Cecilia Lozano, San Isidro Pathology, Province of Buenos Aires, Argentina

    Medical Pathologist, Director of San Isidro Pathology

References

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III. Jaramillo-Santos MA, Sánchez-Gil A, Valencia-Uribe A, Arango-Molano L. Dermatomiositis y cáncer colorrectal: reporte de caso y revisión de la literatura. Rev Colomb Gastroenterol. 2021;36:91-97.

IV. Bohan A, Peter J, Bowman R, Pearson C. Computer-assisted analysis of 153 patients with polymyositis and dermatomyositis. Medicine. 1977;56:255-286.

V. Ito A, Funasaka Y, Shimoura A, Horikawa T, et al. Dermatomyositis associated with diffuse dermal neutrophilia. Int J Dermatol. 1955;34:797-798.

VI. Owen CE, Malone JC, Callen JP. Sweet-like Dermatosis in 2 patients with clinical features of dermatomyositis and underlying autoimmune disease. Arch Dermatol. 2008;144:1486-1490.

VII. Laga A, Larson A, Granter S. Histopathologic spectrum of connective tissue diseases commonly affecting the skin. Surg Pathol Clin. 2017;10:477-503.

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Published

2026-04-28

Issue

Section

Clinical Cases