Pseudoxanthoma elasticum-like papillary dermal elastolysis

Authors

  • Belén Coba Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina
  • María Inés Hernández Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina
  • Julieta Villarroel Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina
  • Leandro Danze Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina
  • Vicenta Neglia Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina

DOI:

https://doi.org/10.47196/ynk7pb72

Keywords:

papillary dermal elastolysis, pseudoxanthoma

Abstract

Papillary dermal elastolysis resemble pseudoxanthoma elasticum (PDERP) is part of a group of diseases affecting the fibroelastic system of the dermis, characterized by a decrease or loss of elastic fibers at different levels, papillary and reticular. It presents as localized skin lesions on the posterior and lateral sides of the neck, flexor surfaces of the forearms, axillae, and lower abdomen, which clinically resemble pseudoxanthoma elasticum (PXE). The age of onset, histopathological findings, and systemic involvement help differentiate these two conditions. We report a case in a 70-year-old woman with typical lesions and distribution.

Author Biographies

  • Belén Coba, Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina

    Medical Student, Specialist in Dermatology Program, University of Buenos Aires (UBA)

  • María Inés Hernández, Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina

    Plant Doctor

  • Julieta Villarroel, Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina

    Plant Doctor

  • Leandro Danze, Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina

    Medical Consultant of the Pathology Department

  • Vicenta Neglia, Dr. Cosme Argerich General Hospital, City of Buenos Aires, Argentina

    Head of the Dermatology Unit

References

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VIII. Murshidi R, Bani Hamad S, Al-Tarawneh A. Pseudoxanthoma elasticum-like papillary dermal elastolysis; A report of two cases and a literature review. Dermatol Online J. 2024; 30.

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Published

2026-04-28

Issue

Vol. 32 No. 1 (2026): January-april

Section

Clinical Cases

License

Copyright (c) 2026 on behalf of the authors. Reproduction rights: Argentine Dermatology

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